International Journal of Speech and Audiology
2025, Vol. 6, Issue 2, Part A
From cochlear microphonics to cortical silence: Audiological progression in auditory neuropathy spectrum disorder
Author(s): Mathew Nishanth A, Anusha Rao S, Jaya Lakshmi PB and A Nandhithaa Meenakshi
Abstract: Auditory Neuropathy Spectrum Disorder (ANSD) is a sensorineural hearing loss characterized by impaired neural synchrony despite preserved outer hair cell function. It presents with absent or abnormal Auditory Brainstem Response, present otoacoustic emissions, and cochlear microphonics. This case study reports a 22-year-old female with progressive Auditory Neuropathy Spectrum Disorder. Initial testing showed minimal hearing loss, robust otoacoustic emissions, present cochlear microphonics, and intact cortical responses. During the follow up testing, the patient’s speech perception scores declined, acoustic reflexes and cortical responses were absent indicating deterioration in the central auditory system. The case highlights the importance of comprehensive audiological assessment including cortical measures, in diagnosing and managing the progressive Auditory Neuropathy Spectrum Disorder.
DOI: 10.22271/27103846.2025.v6.i2a.81
Pages: 19-21 | Views: 233 | Downloads: 111
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How to cite this article:
Mathew Nishanth A, Anusha Rao S, Jaya Lakshmi PB and A Nandhithaa Meenakshi. From cochlear microphonics to cortical silence: Audiological progression in auditory neuropathy spectrum disorder. International Journal of Speech and Audiology. 2025; 6(2): 19-21. DOI: 10.22271/27103846.2025.v6.i2a.81
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